Familial Apical Hypertrophic Cardiomyopathy With Atrioventricular Block

Document Type: Case Report

Authors

1 Rajaie Cardiovascular, Medical, and Research Center, Iran University of Medical Sciences, Tehran, IR Iran.

2 Cardiac Electrophysiology Research Center, Rajaie Cardiovascular, Medical, and Research Center, Iran University of Medical Sciences, Tehran, IR Iran.

Abstract

A 53-year-old woman was referred to us with frequent episodes of palpitation, near-syncope, and dizziness. The patient had a history of apical hypertrophic cardiomyopathy in her sister and aborted sudden cardiac death in her aunt. Because of first-degree atrioventricular block and high atrioventricular Wenckebach point, cardiac magnetic resonance imaging was done, and apical hypertrophic cardiomyopathy was diagnosed. (Iranian Heart Journal 2020; 21(2): 90-93)

Keywords


1. Roberto Barriales-Villa a, Raúl Centurión-Inda a, Xusto Fernández-Fernández a, Martín F. Ortiz a, Luisa Pérez-Álvarez b, Isabel Rodríguez García a, Manuel Hermida-Prieto a, Lorenzo MonserratSevere Cardiac Conduction Disturbances and Pacemaker Implantation in Patients With Hypertrophic Cardiomyopathy Rev Esp Cardiol. 2010;63:985-8 - Vol. 63 Num.08 DOI: 10.1016/S1885-5857(10)70192-4.
2. Islamiyat J. Babs Animashaun, Fitzgerald M. Shepherd, Thiru V. Chinnadurai, Oyeladun Oyenuga, Patrick Odia, Damian Kurian, Aubrey ClarkeAtypical Presentation and Management of Hypertrophic Cardiomyopathy with Atrioventricular Conduction Abnormality Med Sci Case Rep 2016; 3:82-85.
3. Kaneshige T1, Machida N, Itoh H, Yamane Y. The anatomical basis of complete atrioventricular block in cats with hypertrophic cardiomyopathy.
4. K L Rosen, R W Cameron, P J Bigham, and S R NeishHypertrophic cardiomyopathy presenting with 3rd-degree atrioventricular block Tex Heart Inst J. 1997; 24(4): 372–375.
5. Özlem KARAKURTa, Asuman BİÇERa, Ramazan AKDEMİRa, Harun KILIÇaaClinic of Cardiology, Dışkapı Yıldırım Beyazıt Education and Research Hospital, Apical Hypertrophic Cardiomyopathy Associated with High Degree Atrioventricular Block: Case Report Turkiye Klinikleri J Cardiovasc Sci. 2010;22(3):352-4.
6. Z Alizadeh-Sani, S Madadi, A Sadeghpour, Z Khajali, P Golnari, M KiavarCardiac MRI in a patient with coincident left ventricular non-compaction and hypertrophic
cardiomyopathy, The journal of Tehran Heart Center, 2011, 6 (4)214.
7. S Madadi, Z Emkanjoo, J Shahabi, H PourAliakbar Left Ventricular Apical Aneurysm and Ventricular Tachycardia in a Patient With Bicuspid Aortic Valve and Hypertrophic Cardiomyopathy, Iranian heart journal, 2018,19 (4), 58-61.
8. Hoey E.T., Teoh J.K., Das I., Ganeshan A., Simpson H., Watkin R.W. The emerging role of cardiovascular MRI for risk stratification in hypertrophic cardiomyopathy, Clin Radiol 2014; 69 : 221-230.
9. Kim K.H., Yang D.H., Kim C.Y., and al. Recurrent syncope episodes and exercise intolerance in hypertrophic cardiomyopathy combined with atrioventricular conduction disturbance J Cardiovasc Ultrasound 2013; 21 : 148-151.
10. Syed Wamique Yusuf, Jaya D Bathina, Jose Banchs, Elie N Mouhayar, and Iyad N Daher Apical hypertrophic cardiomyopathyWorld J Cardiol. 2011 Jul 26; 3(7): 256–259.
11. Mostafa Ahmadi; Ramin Khameneh BagheriApical Hypertrophic Cardiomyopathy in a Case with Chest Pain and Family History of Sudden Cardiac Death: A Case Report Volume 5, Issue 3, Summer 2017, Page 198-200, 2018.
12. Majid Kyavar, Somayeh Mohammadi, Shabnam Madadi Relationship between syncope and sudden cardiac death in patients with hypertrophic cardiomyopathy and left ventricular mass index calculated by magnetic resonant imaging, Iranian heart journal,2015, 16,(1)12-19.