Cor Triatriatum Dextrum in a Pregnant Woman Combined With an Atrial Septal Defect and Severe Pulmonary Hypertension: A Rare Case Report

Document Type : Case Report


1 Emergency Medicine Department, Mogadishu Somali-Turkish Training and Research Hospital, Mogadishu, Somalia.

2 Cardiology Department, Mogadishu Somali-Turkish Training and Research Hospital, Mogadishu, Somalia.


Cor triatriatum, first described by Church in 1868, is an extremely rare congenital cardiac defect and accounts for between 0.1% and 0.4% of all congenital cardiac anomalies. Isolated cor triatriatum is rare and is usually associated with other cardiac anomalies, most commonly the atrial septal defect (ASD). Although the clinical presentations of cor triatriatum depend on the size of the fenestration, almost all cases are diagnosed in childhood and very few cases remain asymptomatic until adulthood. Several techniques such as transthoracic echocardiography, transesophageal echocardiography, computed tomography, and magnetic resonance imaging are used for the diagnosis of cor triatriatum; nevertheless, the definitive diagnosis and the identification of the associated anomalies can be easily made by echocardiography. The use of computed tomography is associated with the risk of radiation, and transesophageal echocardiography has the discomfort of scope intubation. 5
We herein describe a 35-year-old pregnant woman with no previously described cardiac disorder who was diagnosed with cor triatriatum dextrum presenting with shortness of breath, tachycardia, and palpitation of 1 week’s duration. She had a history of 5 uncomplicated vaginal deliveries. (Iranian Heart Journal 2020; 21(4): 131-134)






  1. Bassareo PP, Tumbarello R, Mercuro G. Cor triatriatum and lipomatous hypertrophy of the interatrial septum in the elderly : a case report. 2010; 1–5.
  2. Malik A, Facc DF, Mohani A, Facc MF, Yekta A. Cor triatriatum : A multimodality imaging approach. 2008; 24(3):2007–8.
  3. Case report : late presentation of symptomatic cor triatriatum sinistrum. 2010; 2010.
  4. Kokotsakis J, Anagnostakou V, Almpanis G, Paralikas I, Nenekidis I, Kratimenos T, et al. Cor triatriatum presenting as heart failure with reduced ejection fraction : a case report. 2011; 2–5.
  5. Bai W, Kaushal S, Malviya S, Griffith K, Ohye RG. Anesthetic management for resection of cor triatriatum during the second trimester of pregnancy. Int J Obstet Anesth [Internet]. 2009; 19(1):103–6. Available from:
  6. Nabais S, Salomé N, Brandão A, Simões A, Marques J, Costa J, et al. Coexistence of coronary cameral fistulae and cor triatriatum sinister in an elderly patient. Eur J Echocardiogr. 2008; 9(5):712–5.