Document Type : Case Report
Department of Interventional Cardiology, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, IR Iran.
Cardiovascular Research Center, Institute of Basic and Clinical Physiology Sciences, Kerman University of Medical Sciences, Kerman, IR Iran.
Pulmonary agenesis is a very rare congenital disorder with a chromosome recessive inheritance. Half of the cases with pulmonary agenesis suffer from other congenital disorders such as cardiovascular, skeletal, and gastrointestinal defects. Clinical manifestations vary from respiratory problems to recurrent chest infections, which occur in different stages of life including infancy, childhood, and adolescence. The mortality rate of pulmonary agenesis is about 50% among neonates, especially if it is associated with other disorders like cardiac anomalies. In this paper, we report a case of left-sided lung agenesis in a 32-year-old woman. (Iranian Heart Journal 2021; 22(4): 135-139)