Iranian Heart Journal

Iranian Heart Journal

Introducing a Rare Case: Unilateral Absence of the Pulmonary Artery Branch Associated With Large Patent Ductus Arteriosus in an Adult Patient

Document Type : Case Report

Authors
Mozhgan Parsaei 1
Zahra Khajali 2
Raheleh Kaviani 1
Hamidreza Pouraliakbar 2
Melody Farrashi 1
Farnoosh Larti 3
1 Echocardiography Research Center, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, IR Iran.
2 Rajaie Cardiovascular, Medical, and Research Center, Iran University of Medical Sciences, Tehran, IR Iran.
3 Tehran University of Medical Sciences, Tehran, IR Iran.
Abstract
Unilateral absence of the pulmonary artery (UAPA) is a rare congenital cardiovascular anomaly with a wide array of symptoms. An 18-year-old man was referred to our hospital with dyspnea on exertion and central cyanosis. Transthoracic and transesophageal echocardiographic examinations revealed severe right ventricular enlargement, large main and left pulmonary arteries, severe pulmonary hypertension, and a large patent ductus arteriosus (PDA). The right pulmonary artery could not be seen; consequently, UAPA was considered. Computed tomography angiography confirmed the diagnosis. Our case is a rare condition with UAPA associated with patent ductus arteriosus, diagnosed in adulthood. It underscores the need for awareness of this anomaly for early diagnosis and treatment. (Iranian Heart Journal 2022; 23(4): 125-130)
Keywords
Unilateral absence of pulmonary artery
Patent ductus arteriosus
Pulmonary hypertension
Congenital heart disease
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Iranian Heart Journal
Volume 23, Issue 4
Autumn 2022
Pages 125-130