Rajaie Cardiovascular Medical and Research Institute, Iran University of Medical Sciences, Tehran, IR Iran.
Abstract
Tetralogy of Fallot (TOF) is one of the most common congenital heart diseases. Family recurrence provides strong evidence for the involvement of a genetic component in the susceptibility to TOF. The role of genetic factors is supported by the increased risk of first-degree relatives of patients with TOF. The clinical course of this disease is unclear and unpredictable. We herein describe 2 siblings suffering from TOF with left ventricular noncompaction cardiomyopathy (LVNC) and their clinical course and treatment. LVNC is a rare disease known by prominent trabeculation of the ventricles and reduced systolic function. LVNC can manifest itself in a wide spectrum of symptoms overlapping with other cardiac diagnoses. Familial patterns of disease development and coexistence of cardiac abnormalities are also reported. (Iranian Heart Journal 2024; 25(1): 98-105)
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Abbaszadeh, R., Naderi, F., Tatari, H., & Tolouei Tabar, Y. (2024). Left Ventricular Noncompaction Cardiomyopathy in 2 Siblings With Underlying Tetralogy of Fallot: A Case Report. Iranian Heart Journal, 25(1), 98-105.
MLA
Reza Abbaszadeh; Fatemeh Naderi; Hassan Tatari; Yaser Tolouei Tabar. "Left Ventricular Noncompaction Cardiomyopathy in 2 Siblings With Underlying Tetralogy of Fallot: A Case Report". Iranian Heart Journal, 25, 1, 2024, 98-105.
HARVARD
Abbaszadeh, R., Naderi, F., Tatari, H., Tolouei Tabar, Y. (2024). 'Left Ventricular Noncompaction Cardiomyopathy in 2 Siblings With Underlying Tetralogy of Fallot: A Case Report', Iranian Heart Journal, 25(1), pp. 98-105.
VANCOUVER
Abbaszadeh, R., Naderi, F., Tatari, H., Tolouei Tabar, Y. Left Ventricular Noncompaction Cardiomyopathy in 2 Siblings With Underlying Tetralogy of Fallot: A Case Report. Iranian Heart Journal, 2024; 25(1): 98-105.
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