AORTIC SURGERY IN A PATIENT WITH MARFAN SYNDROME AND PECTUS EXCAVATUM

Authors

1 Associate Professor in Cardiac Surgery, Rajaie Cardiovascular, Medical and Research Center, Tehran University of Medical Sciences, Tehran, Iran

2 Corresponding Author; Professor in Cardiology, Rajaie Cardiovascular, Medical and Research Center, Tehran University of Medical Sciences

3 Assistance Professor in Cardiac Anesthesiology, Rajaie Cardiovascular, Medical and Research Center, Tehran University of Medical Sciences, Tehran, Iran

4 Assistance Professor in Cardiology, Rajaie Cardiovascular, Medical and Research Center, Tehran University of Medical Sciences, Tehran, Iran

Abstract

Severe cardiovascular disorders, including aortic dissection and aneurismal dilation of the aorta, are the main life-threatening complications of the Marfan syndrome 1. Approximately two thirds of individuals who have this syndrome have chest wall deformities such as pectus excavatum or pectus carinatum 2. When a patient with pectus excavatum needs aortic surgery, the surgeon may face a major clinical challenge in choosing the optimal surgical approach 3. We present a case of the Marfan syndrome with severe pectus excavatum who underwent aortic surgery.